Médecine néonatale et pédiatrique

Abstrait

Rapunzel Syndrome in Children

Ghormallah A, Ghannam AA and Al-Olait Y

Rapunzel syndrome is a variety of trichobezoar which has a tail extending down through pylorus to small intestine. Most reported cases were female with underlying psychiatric problem. We are reporting 7 years old girl presented with history of chronic abdominal pain (discomfort), progressive in nature, abdominal distention and weight loss. Radiological work-up is consistent with huge filling defect in stomach. Laparatomy and gastrotomy was done, a huge trichobezoar with a long tail extending to proximal part of small intestine was removed. Post- surgical hospital course was smooth with no complications and she was discharged in the 2nd week, given a follow up with psychiatrist and psychologist for evaluation and management to prevent recurrence