Médecine néonatale et pédiatrique

Abstrait

Moya Moya Disease in a 5 Year Child-presenting as Hemiparesis withMedullary Sponge Kidneys

Rahul Gandhi, Jitender and Vineet Anand

Moya moya disease is a very rare cause of acute stroke in pediatrics age group. The disease was first described by Takeuchi and Shmuziin 1957.since the disease is common in japan and cases have been reported mostly in japan but cases have been reported rarely from non-Japanese regions including India. Moya moya disease is a progressive steno occlusive disease at terminal portion of internal carotid arteried with development of collateral channels of circulation.

We report a case of 5 years male child who presented with history of fall 1 day back followed by sudden loss of speech and weakness of right side of the body. Patient was diagnosed moya moya disease on basis of MRI angiography.