Médecine néonatale et pédiatrique

Abstrait

Dental Considerations in Dandy-Walker Malformation

Rungnapa Warotayanont, Samuel Huang, Ram Vaderhobli, Juei Kao and Thuan Le

Dandy-Walker malformation is a rare congenital cystic malformation of the posterior cranial fossa. Patients with Dandy-Walker malformation show signs and symptoms of complex clinical manifestations, ranging from cranial nerve and cerebellar dysfunctions to extracranial abnormalities, which may pose challenges in dental management. In the current report, an 11 year-old boy with Dandy-Walker malformation presented with fracture of previously root canal-treated right maxillary central incisor. He was developmentally delayed, hearing and visually impaired, and presented with ataxic gait. Following clinical examination and behavioral assessment, dental treatments including gingivectomy, fiber post bonding and coronal restoration were planned and completed under the use of oral sedative medications. Patient tolerated the procedure well with no complications during and after the treatment. Despite the complexity of Dandy-Walker malformation, the careful review of medical history and proper behavioral assessment suggests that dental treatment can be achieved in the dental chair.