Médecine néonatale et pédiatrique

Abstrait

Amniotic Band Syndrome with Craniofacial Region Deformity - A Case Report

Solomon Gebre, Ermias Abate and Awol Yeman

Amniotic band syndrome is one of the uncommonly seen congenital deformity that can lead to a wide range of structural abnormalities mostly involves limbs but may affect the craniofacial region and trunk. In this report, we describe the case of A 30 years old Gravida 4 Para 3 who presented at gestational age of 28+4 weeks for Antenatal care follow up at Mearg general hospital, in Northern Ethiopia. The pregnancy was terminated after ultrasound showed a severely malformed fetus. Amniotic band syndrome is seen very uncommonly, but there should be high clinical suspicion in the presence of congenital deformity. In a setup where ultrasound is ready available Amniotic band syndrome can be diagnosed intrapartum, otherwise the defects are seen in the postpartum period. Surgical treatment with an Interdisciplinary approach to every single case is the main stay of therapy in managing Amniotic band syndrome. Fetus with deformities that are incompatible with extra uterine life, pregnancy should be terminated after informed consent is collected. We therefore report a case seen with the aim of highlighting its existence in this region and to point out diagnostic and therapeutic approaches inn pregnancy with Amniotic band syndrome in a low resource setting through this case report.